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  • 产品名称:ALDH6A1 抗原(重组蛋白)

  • 产品型号:100ug
  • 产品厂商:通蔚生物
  • 产品价格:800
  • 产品库存:35
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详情介绍:

中文名称: ALDH6A1 抗原(重组蛋白)

英文名称: ALDH6A1 Antigen (Recombinant Protein)

别     名:  aldehyde dehydrogenase 6 family, member A1; MMSDH; MMSADHA

储     存:  冷冻(-20℃)

相关类别: 抗原

概     述:

Fusion protein corresponding to C terminal 250 amino acids of human ALDH6A1
    
技术规格

Full name:

aldehyde dehydrogenase 6 family, member A1

Synonyms:

MMSDH; MMSADHA

Swissprot:

Q02252

Gene Accession:

BC004909

Purity:

>85%, as determined by Coomassie blue stained SDS-PAGE

Expression system:

Escherichia coli

Tags:

His tag C-Terminus, GST tag N-Terminus

Background:

This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.





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